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Question-First Step 1 Biochemistry Practice
Free USMLE Step 1 Biochemistry Practice Questions
See the free-preview topics and major foundational science areas covered by BiochemStep, then start the free 20-question Step 1-style practice set.
Free preview includes
Topics represented in the 20-question free preview
Amatoxin inhibition of RNA polymerase IIAspirin and irreversible cyclooxygenase inhibitionClassic PKU (phenylalanine hydroxylase deficiency)Classic PKU (phenylalanine hydroxylase deficiency)Classic PKU (phenylalanine hydroxylase deficiency)Cyanide poisoningELISA antigen or antibody detectionFamilial hypercholesterolemiaFolate deficiencyG6PD deficiencyLesch-Nyhan syndrome (HGPRT deficiency)Lesch-Nyhan syndrome (HGPRT deficiency)MCAD deficiencyPCR primer amplification / target DNA detectionRefeeding syndrome diagnosisTay-Sachs disease (hexosaminidase A)Tay-Sachs disease (hexosaminidase A)Vitamin B12 deficiencyVon Gierke diseaseXeroderma pigmentosum due to defective nucleotide excision repair
Coverage by foundational science area
Major topic areas covered
Amino Acid Metabolism
Bilirubin Metabolism DisordersBranched-Chain Amino Acid Metabolism DisordersHomocystinuriaPhenylalanine Metabolism DisordersPorphyrin and Heme Synthesis DisordersTryptophan and Niacin MetabolismTyrosine Metabolism DisordersUrea Cycle Disorders
Carbohydrate Metabolism
Alcohol MetabolismDisaccharide MetabolismFructose MetabolismGalactose MetabolismGlucokinase / MODYGlucose Metabolism RegulationGlycation and Glucose MonitoringGlycogen Storage DiseasesGlycolysis DisordersMitochondrial Toxicity and Oxidative PhosphorylationPDH ComplexPentose Phosphate PathwayPolyol PathwayThiamine-Dependent Metabolism
Enzyme Kinetics
Competitive vs noncompetitive vs uncompetitiveDigestive enzyme activationEnzyme Deficiencies and Pharmacologic ToxicityEnzyme KineticsGlucokinase / MODYSuicide inhibitors / irreversible inhibition
Genetics & Cell Biology
Amino Acid Transport DisordersApoptosis and Cell SignalingCell SignalingChromosomal AneuploidiesCollagen and Connective Tissue DisordersCystic Fibrosis and CFTRDNA Repair DisordersEmbryology and Developmental PatterningGenomic Imprinting DisordersInheritance PatternsLysosomal Storage DiseasesMembrane Transport and Ion GradientsMitochondrial GeneticsMucopolysaccharidosesOncogene and Tumor Suppressor SignalingPopulation GeneticsSphingolipidosesTrinucleotide Repeat DisordersTumor Suppressor and Oncogene Mechanisms
Immunology & Hematologic Mechanisms
Antigen Processing and PresentationB-Cell Development and Primary ImmunodeficiencyCoagulation Regulation and HypercoagulabilityComplement Deficiencies and Bacterial DefenseComplement Regulation and AngioedemaCytokine Signaling and Granuloma MaintenanceHemoglobin and Red Cell DisordersLymphocyte Development and Antibody DiversificationLymphocyte Development and Receptor DiversityOxidative Burst and Phagocyte FunctionPhagocyte Adhesion and Innate Immune DefectsPhagocyte Function and Vesicle Trafficking DisordersT-Cell Activation and Immunosuppressive SignalingT-Cell Regulation and Immune Checkpoints
Integrated Metabolism & Physiology
Acid-Base PhysiologyDigestive Enzyme ActivationDrug Metabolism and Toxic MetabolitesFasting, Starvation, and GluconeogenesisHemoglobin Biochemistry and Oxygen TransportIron Metabolism and Hepcidin RegulationMembrane Transport and Ion GradientsOxidative PhosphorylationRenal Acid-Base PhysiologySignal Transduction and Cytoskeletal PharmacologySignal Transduction and Receptor Biology
Lab Techniques
Cytogenetic TechniquesGene Editing TechniquesImmunologic and Protein Detection TechniquesMolecular Diagnostic TechniquesSeparation Techniques
Lipid Metabolism
Cholesterol Synthesis and LDL Receptor RegulationDiabetic KetoacidosisFatty Acid Oxidation and TransportFatty Acid Synthesis and RegulationKetone Body MetabolismLipoprotein Metabolism DisordersMetabolic Pathway PharmacologyOdd-Chain Fatty Acid and Propionate Metabolism
Molecular Biology
Chromatin and Epigenetic RegulationCollagen and Connective Tissue DisordersDNA Repair and Cancer TherapyProtein Folding and MisfoldingProtein Structure and MisfoldingRNA Processing and Gene ExpressionTelomeres and Genome MaintenanceToxin-Mediated Inhibition of Protein SynthesisTranscription and TranslationTrinucleotide Repeat Disorders
Nucleotide Metabolism
Antiviral Nucleotide AnalogsAspirin PharmacologyDrug Metabolism and PharmacogenomicsFolate Antimetabolites and RescueMicrobial Diagnostic ReasoningPurine MetabolismPyrimidine and Purine AntimetabolitesPyrimidine MetabolismTranslation and Protein Synthesis InhibitorsVitamin B6 and Heme Synthesis
Nutrition
Niacin DeficiencyProtein-Energy MalnutritionRefeeding SyndromeThiamine DeficiencyTrace Elements and Micronutrients
Vitamins & Cofactors
Copper Metabolism DisordersFat-Soluble VitaminsIron Metabolism and Hepcidin RegulationWater-Soluble Vitamins