What this page covers
Practice Step 1-style biochemistry questions on CFTR potentiator mechanism (ivacaftor), including CF with gating mutation, genotype-directed therapy added, mechanism, with emphasis on clinical behavior / pharmacology and answer-choice reasoning.
How to use this page
Review the topic and reasoning focus, then practice Step 1-style questions inside BiochemStep. The question set emphasizes mechanism-first answer-choice reasoning rather than passive content review.